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  • © 2017

Pulmonary Hypertension in Adult Congenital Heart Disease

  • Explains all aspects of pulmonary hypertension diagnosis
  • Describes management options and related issues, including in patient subsets
  • Will serve as a comprehensive, practically oriented reference

Part of the book series: Congenital Heart Disease in Adolescents and Adults (CHDAA)

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eBook USD 89.00
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Softcover Book USD 119.99
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Hardcover Book USD 169.99
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  • Durable hardcover edition
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Table of contents (24 chapters)

  1. Front Matter

    Pages i-xv
  2. Pathophysiology and Classification of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter

      Pages 1-1
    2. Congenital Heart Defects and Pulmonary Hypertension: The Heath–Edwards Paradigm

      • Konstantinos Dimopoulos, Elizabeth Orchard, Annalisa Angelini
      Pages 3-22
    3. Pulmonary Arterial Hypertension in Patients with Previous Reparative Surgery

      • Shahin Moledina, Paraskevi Theocharis
      Pages 61-68
    4. Segmental Pulmonary Hypertension

      • Konstantinos Dimopoulos, Claudia Montanaro, Gerhard-Paul Diller
      Pages 69-89
    5. Pulmonary Vascular Disease in Patients with Fontan-Type Circulation

      • Lars Idorn, Lars Søndergaard
      Pages 91-104
    6. Post-capillary Pulmonary Hypertension in ACHD

      • Margarita Brida, Gerhard-Paul Diller
      Pages 105-117
  3. The Diagnosis of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter

      Pages 119-119
    2. The Role of Plain Chest Radiography and Computed Tomography

      • Edward D. Nicol, Michael B. Rubens
      Pages 149-161
    3. Cardiovascular Magnetic Resonance

      • Michael A. Quail, Sonya V. Babu-Narayan
      Pages 179-193
    4. Cardiopulmonary Exercise and Six-Minute Walk Testing

      • Graham Stuart, Reza Ashrafi
      Pages 195-214
    5. Cardiac Catheterization

      • Massimo Chessa
      Pages 215-226
  4. Management of Pulmonary Hypertension in Adult Congenital Heart Disease

    1. Front Matter

      Pages 227-227
    2. Conservative Management and Recommendations for Pulmonary Arterial Hypertension Related to Congenital Heart Disease

      • Heba Nashat, Samantha J. Fitzsimmons, Carl Harries, Konstantinos Dimopoulos, S. John Wort
      Pages 229-251

About this book

This book is intended as a comprehensive, practically oriented reference on pulmonary hypertension within the context of adult congenital heart disease (ACHD). After an introductory chapter on pathophysiology, the various types of pulmonary hypertension that may be encountered in ACHD are discussed, highlighting the specifics observed within different patient categories. The diagnostic approach is then addressed in detail, and the last section of the book is devoted to management options, from conservative approaches to interventional treatment and the concept of treat and repair. Management in specific patient subjects, such as pregnant women, Fontan patients, and Down syndrome patients with Eisenmenger syndrome, is fully discussed, and guidance is also provided on palliative care.

Pulmonary arterial hypertension related to congenital heart disease (PAH-CHD), despite significant similarities in lung pathohysiology, differs significantly from other types of PAH in terms of mechanism of onset, natural history and management. Mistakes and pitfalls in the management of patients with PAH-CHD are often related to a lack of knowledge or expertise in this condition. Pulmonary Hypertension in Adult Congenital Heart Disease will be a valuable resource and learning tool for all who care for patients with ACHD, both in tertiary practice and general cardiology.

Editors and Affiliations

  • Adult Congenital Heart Centre and Centre for Pulmonary Hypertension, Royal Brompton Hospital and Imperial College, London, United Kingdom

    Konstantinos Dimopoulos

  • University Hospital, Münster, Germany

    Gerhard-Paul Diller

About the editors

Diller Gerhard, Royal Bromption Hospital, London, UK

Konstantinos Dimopoulos, Royal Bromption Hospital, London, UK

Bibliographic Information

  • Book Title: Pulmonary Hypertension in Adult Congenital Heart Disease

  • Editors: Konstantinos Dimopoulos, Gerhard-Paul Diller

  • Series Title: Congenital Heart Disease in Adolescents and Adults

  • DOI: https://doi.org/10.1007/978-3-319-46028-4

  • Publisher: Springer Cham

  • eBook Packages: Medicine, Medicine (R0)

  • Copyright Information: The Editor(s) (if applicable) and The Author(s), under exclusive license to Springer Nature Switzerland AG 2017

  • Hardcover ISBN: 978-3-319-46026-0Published: 22 September 2017

  • Softcover ISBN: 978-3-319-83424-5Published: 10 August 2018

  • eBook ISBN: 978-3-319-46028-4Published: 08 September 2017

  • Series ISSN: 2364-6659

  • Series E-ISSN: 2364-6667

  • Edition Number: 1

  • Number of Pages: XV, 368

  • Number of Illustrations: 36 b/w illustrations, 46 illustrations in colour

  • Topics: Cardiology, Cardiac Surgery, Pneumology/Respiratory System

Buy it now

Buying options

eBook USD 89.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book USD 119.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info
Hardcover Book USD 169.99
Price excludes VAT (USA)
  • Durable hardcover edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Other ways to access