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Cystic Fibrosis in Primary Care

An Essential Guide to a Complex, Multi-System Disease

  • Written by a family medicine physician who has specialist level experience with Cystic Fibrosis
  • Written specifically for the family medicine practitioner to help broaden their understanding of how the disease affects the patient globally
  • Organized under headings that correspond to major components of Cystic Fibrosis as opposed to a more standard approach of diagnosis, epidemiology, testing, treatment, etc

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Table of contents (15 chapters)

  1. Front Matter

    Pages i-xiv
  2. Evolution of Cystic Fibrosis Care

    • Douglas Lewis, Natalie Sollo, Philip Black
    Pages 1-7
  3. CF Basics

    • Natalie Sollo, Mazahir Ali
    Pages 9-17
  4. CFTR Physiology

    • Apeksha Sathyaprasad
    Pages 19-25
  5. Spirometry in Cystic Fibrosis

    • Donald Seery, Lary Hill
    Pages 27-39
  6. Exercise for CF

    • Maurice Duggins, Douglas Lewis
    Pages 41-46
  7. Inflammation in Cystic Fibrosis

    • Rex B. Keith, Douglas Lewis
    Pages 47-56
  8. CF Airway Clearance

    • Dee Ann Bragg, Douglas Lewis
    Pages 57-67
  9. Acute and Chronic Infection Management in CF

    • Patrick Allen, Joseph Borick, Jamie Borick
    Pages 69-87
  10. Sexual and Reproductive Health and Counseling

    • Lisa Gilbert, Sara Johnson, Sarah Stokes
    Pages 89-104
  11. Gastrointestinal Disease and Nutrition in Cystic Fibrosis

    • Sheryl Beard, Margaret Pray
    Pages 105-116
  12. CF Related Diabetes

    • Douglas Lewis, Melissa C. Norton, Lyndsey N. Buzzard
    Pages 117-125
  13. Electrolyte Abnormalities in CF

    • Jennifer Wipperman, Jackie Anderson
    Pages 127-139
  14. CFTR Carrier Status

    • Bonnie Tibbe, Craig Cunningham
    Pages 141-151
  15. CFTR Corrector Therapies/New Therapies

    • Douglas Lewis
    Pages 153-159
  16. Psychology and Psychotherapy in CF

    • Ruth Nutting, Stephen Amos
    Pages 161-176
  17. Back Matter

    Pages 177-182

About this book


Cystic fibrosis is a disease that affects the entire body. It tends to be thought of as primarily a pulmonary disease since pulmonary decline is the main factor in early mortality. Because of the multi-system nature of the disease, a better understanding of cystic fibrosis expands the family physician's understanding of subjects ranging from genetics to pulmonary function to nutrition to colon transport to hydration to electrolyte management. The primary care philosophy is unique in that it always considers how a narrow problem can affect an individual globally. Cystic Fibrosis care can often feel fractured to patients as they are sent to multiple specialists to deal with problems outside of the comfort level of a prior or current specialist. With a broad medical philosophy, care is more inclusive as clinicians can manage topics such as diabetes and preventive care without multiple referrals and additional appointments. Family physicians are well-positioned and well-qualified to competently meet many of the care needs of those with cystic fibrosis.

This book is edited by a family medicine physician who has specialist level experience with the disease. It opens with a background on cystic fibrosis foundations and centers to familiarize the reader. The next chapter gives a basic overview of the disease. Each of the subsequent chapters provide a comprehensive look at how cystic fibrosis affects other areas of the body that the primary care physician should be familiar with. Major components of cystic fibrosis such as physiology, spirometry, inflammation, airway clearance, chronic infection, cystic fibrosis related diabetes and pancreatic insufficiency, among others, are thoroughly explained. 

 

Written by experts in the field, Cystic Fibrosis in Primary Care appeals to all family physicians as well as specialists, residents, medical students physician assistants and nurse practitioners alike.

     


Editors and Affiliations

  • St. Joseph Family Medicine Clinic, Via Christi Regional Medical Center, Wichita, USA

    Douglas Lewis, MD, FAAFP

About the editor

Douglas Lewis, MD, FAAFP

Via Christi Regional Medical Center

St. Joseph Family Medicine Clinic

Wichita, Kansas, USA


Dr. Lewis is a family practitioner at Via Christi St. Joseph Family Medicine Clinic. His interest in cystic fibrosis began in 2008 from personal experience. At this time, the adult Cystic Fibrosis clinic at his institution had been shut down. The clinic administrator knew of Dr. Lewis' research on cystic fibrosis and asked him to consider joining one of the pulmonologists who had interest in re-establishing the adult clinic. Dr. Lewis accepted and has been co-operating the Via Christi Adult CF Specialty Clinic since 2011. He is also a clinical assistant professor at the University of Kansas School of Medicine-Wichita. He teaches in the department of family and community medicine.  

        



Bibliographic Information

  • Book Title: Cystic Fibrosis in Primary Care

  • Book Subtitle: An Essential Guide to a Complex, Multi-System Disease

  • Editors: Douglas Lewis, MD, FAAFP

  • DOI: https://doi.org/10.1007/978-3-030-25909-9

  • Publisher: Springer Cham

  • eBook Packages: Medicine, Medicine (R0)

  • Copyright Information: Springer Nature Switzerland AG 2020

  • Softcover ISBN: 978-3-030-25908-2Published: 29 January 2020

  • eBook ISBN: 978-3-030-25909-9Published: 28 January 2020

  • Edition Number: 1

  • Number of Pages: XIV, 182

  • Number of Illustrations: 2 b/w illustrations, 17 illustrations in colour

  • Topics: Primary Care Medicine, Pneumology/Respiratory System, General Practice / Family Medicine

Buy it now

Buying options

eBook USD 39.99
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book USD 54.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Other ways to access