Auto-Inflammatory Syndromes
Pathophysiology, Diagnosis, and Management
Editors: Efthimiou, Petros (Ed.)
Free Preview- Provides thorough, up-to-date information and clinical applications for auto-inflammatory syndromes
- Includes basic science and pathophysiology of these diseases to inform clinical decision making
- Covers rare and rarely documented diseases in adults and pediatric patients, including systemic idiopathic arthritis, still’s disease, papa syndrome, and sweets syndrome
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- About this book
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This book provides an overview of auto-inflammatory syndromes, covering the underlying immune mechanisms that lead to their development, specific disease presentations, and clinical treatment guidelines. The book is divided into two sections, adult and pediatric, with chapters focusing on individuals diseases such as systemic arthritis, hyper-IgD, pap syndrome, idiopathic recurrent pericarditis, and familial Mediterranean fever. Chapters incorporate the most recent advances in disease pathophysiology and examine the underlying inductive and effector mechanisms and therapies that relate to each auto-inflammatory disorder at the genetic, molecular, cellular, and epidemiologic levels. The book also discusses the research behind auto-inflammatory disorders to offer detailed clinical guidelines regarding diagnostic techniques, treatment plans, and advice on how to best transition pediatric patients into adult treatment. This is an invaluable reference on auto-inflammatory syndromes for clinicians and researchers in pediatric and adult rheumatology and immunology.
- About the authors
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Petros Efthimiou, MD
Clinical Professor of Medicine
New York University School of Medicine
New York, NY
- Table of contents (22 chapters)
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Immunology of Auto-inflammatory Syndromes
Pages 1-16
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Mevalonate Kinase Deficiency (MKD)/Hyperimmunoglobulin D Syndrome (HIDS)
Pages 19-27
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The TNF Receptor-Associated Autoinflammatory Syndrome (TRAPS)
Pages 29-38
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PAPA Syndrome and the Spectrum of PSTPIP1-Associated Inflammatory Diseases
Pages 39-59
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Blau Syndrome
Pages 61-67
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Table of contents (22 chapters)
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Bibliographic Information
- Bibliographic Information
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- Book Title
- Auto-Inflammatory Syndromes
- Book Subtitle
- Pathophysiology, Diagnosis, and Management
- Editors
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- Petros Efthimiou
- Copyright
- 2019
- Publisher
- Springer International Publishing
- Copyright Holder
- Springer Nature Switzerland AG
- eBook ISBN
- 978-3-319-96929-9
- DOI
- 10.1007/978-3-319-96929-9
- Hardcover ISBN
- 978-3-319-96928-2
- Edition Number
- 1
- Number of Pages
- XIX, 322
- Number of Illustrations
- 8 b/w illustrations, 31 illustrations in colour
- Topics
