Overview
- Offers up-to-date information on the research background and treatment of these pulmonary diseases
- Explores basic molecular biological research as well as clinical applications
- Primarily aimed at researchers and clinicians
Part of the book series: Milestones in Drug Therapy (MDT)
Access this book
Tax calculation will be finalised at checkout
Other ways to access
Table of contents (13 chapters)
-
Etiopathology and Genetics of Rare Lung Diseases
-
Treatment of Cystic Fibrosis
-
Treatment of Other Rare Lung Diseases
Keywords
About this book
This volume describes the pathogenesis and pathophysiology of several pulmonary diseases as well as their treatment. It also discusses the underlying genetic and molecular biological basis, which opens the way for new treatments for these conditions.
It focuses on the treatment of cystic fibrosis including CFTR (cystic fibrosis transmembrane-conductance regulator) modulator therapies, drug therapies that augment airway surface liquid as well as anti-inflammatory and anti-infective therapies. Further topics include long-term, low-dose macrolide therapy for diffuse panbronchiolitis; novel agents for previously untreatable idiopathic pulmonary fibrosis; possible new treatments for pulmonary alveolar proteinosis (PAP); and multiple novel therapeutic targets for treating lymphangiomyomatosis. Research into these conditions has led to major advances in our understanding of the underlying genetic and molecular basis of this disease, and to dramatic improvements in survival and quality of life for affected individuals.
Reviews
Editors and Affiliations
Bibliographic Information
Book Title: Treatment of Cystic Fibrosis and Other Rare Lung Diseases
Editors: Arata Azuma, Michael S. Schechter
Series Title: Milestones in Drug Therapy
DOI: https://doi.org/10.1007/978-3-0348-0977-1
Publisher: Springer Basel
eBook Packages: Biomedical and Life Sciences, Biomedical and Life Sciences (R0)
Copyright Information: Springer International Publishing Switzerland 2017
Hardcover ISBN: 978-3-0348-0975-7Published: 09 February 2017
eBook ISBN: 978-3-0348-0977-1Published: 28 January 2017
Series ISSN: 2296-6056
Series E-ISSN: 2296-6064
Edition Number: 1
Number of Pages: VIII, 263
Number of Illustrations: 19 b/w illustrations, 14 illustrations in colour
Topics: Pharmacology/Toxicology, Pneumology/Respiratory System, Internal Medicine, Immunology