Skip to main content
  • Book
  • © 2015

Orphan Lung Diseases

A Clinical Guide to Rare Lung Disease

  • Contains practical and easy-to-access information on the diagnostic approach, with illustrations of chest imaging (mostly high resolution computed tomography)
  • Assists the reader in evoking and confirming the diagnosis of a variety of orphan diseases
  • Written by experts internationally

Buy it now

Buying options

eBook USD 139.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book USD 179.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Other ways to access

This is a preview of subscription content, log in via an institution to check for access.

Table of contents (36 chapters)

  1. Front Matter

    Pages i-xviii
  2. Orphan Lung Diseases from Definition to Organisation of Care

    • Jean-François Cordier, Vincent Cottin
    Pages 1-3
  3. The Challenges of Clinical Research in Orphan Diseases

    • Paolo Spagnolo, Roland M. du Bois
    Pages 5-15
  4. Chronic Bronchiolitis in Adults

    • Talmadge E. King Jr.
    Pages 17-27
  5. “Diffuse Bronchiectasis of Genetic Origin”

    • Jane S. Lucas, Katharine C. Pike
    Pages 29-51
  6. Allergic Bronchopulmonary Mycosis

    • Isabelle Tillie-Leblond, Jean-François Bervar, Antoine Deschildre
    Pages 53-71
  7. Orphan Tracheopathies

    • Fabien Maldonado, Sara Tomassetti, Jay H. Ryu
    Pages 73-89
  8. Amyloidosis and the Respiratory Tract

    • Christopher P. Venner, Jennifer H. Pinney, Helen J. Lachmann
    Pages 91-111
  9. Granulomatosis with Polyangiitis (Wegener’s Granulomatosis)

    • Christian Pagnoux, Alexandra Villa-Forte
    Pages 127-153
  10. Alveolar Hemorrhage

    • Jason Wells, Stephen K. Frankel
    Pages 155-175
  11. Pulmonary Involvement in Takayasu Arteritis and Behçet Disease

    • Laurent Arnaud, Miguel Hie, Zahir Amoura
    Pages 177-190
  12. Pulmonary Vascular Manifestations of Hereditary Hemorrhagic Telangiectasia

    • Els M. de Gussem, Marie E. Faughnan
    Pages 191-200
  13. Hepatopulmonary Syndrome

    • Karen L. Swanson
    Pages 201-210
  14. Non-langerhans Cell Histiocytosis-Including Erdheim-Chester Disease- and the Lung

    • Julien Haroche, Anne-Laure Brun, Frédérique Capron, Frédéric Charlotte, Philippe A. Grenier, Zahir Amoura
    Pages 211-226
  15. Eosinophilic Pneumonia

    • Vincent Cottin, Jean-François Cordier
    Pages 227-251
  16. Multiple Cystic Lung Diseases

    • Jean-François Cordier, Vincent Cottin, Chahéra Khouatra, Sophie Giraud, Romain Lazor
    Pages 253-270
  17. Lymphangioleiomyomatosis

    • Simon R. Johnson
    Pages 271-283
  18. Pulmonary Alveolar Proteinosis

    • Raphael Borie, Pauline Pradère, Claire Danel, Marie-Pierre Debray, Bruno Crestani
    Pages 285-294
  19. Exogenous Lipoid Pneumonia

    • Anne Gondouin, Jean-Charles Dalphin
    Pages 295-303

About this book

Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides a comprehensive, clinically focused textbook on rare and so-called ‘orphan’ pulmonary diseases. The book is oriented towards the diagnostic approach, including manifestations suggesting the disease, diagnostic criteria, methods of diagnostic confirmation, and differential diagnosis, with an overview of management.

Editors and Affiliations

  • Rare Pulmonary Diseases, Hôpital Louis Pradel, Lyon, France

    Vincent Cottin, Jean-Francois Cordier

  • Respiratory Medicine, University of Southampton, Southampton, United Kingdom

    Luca Richeldi

Bibliographic Information

  • Book Title: Orphan Lung Diseases

  • Book Subtitle: A Clinical Guide to Rare Lung Disease

  • Editors: Vincent Cottin, Jean-Francois Cordier, Luca Richeldi

  • DOI: https://doi.org/10.1007/978-1-4471-2401-6

  • Publisher: Springer London

  • eBook Packages: Medicine, Medicine (R0)

  • Copyright Information: Springer-Verlag London 2015

  • Softcover ISBN: 978-1-4471-6953-6Published: 14 October 2016

  • eBook ISBN: 978-1-4471-2401-6Published: 10 January 2015

  • Edition Number: 1

  • Number of Pages: XVIII, 625

  • Number of Illustrations: 148 b/w illustrations, 100 illustrations in colour

  • Topics: Pneumology/Respiratory System, Internal Medicine

Buy it now

Buying options

eBook USD 139.00
Price excludes VAT (USA)
  • Available as EPUB and PDF
  • Read on any device
  • Instant download
  • Own it forever
Softcover Book USD 179.99
Price excludes VAT (USA)
  • Compact, lightweight edition
  • Dispatched in 3 to 5 business days
  • Free shipping worldwide - see info

Tax calculation will be finalised at checkout

Other ways to access