Behçet's Syndrome

1. Front Matter

   Pages i-x

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2. The Numbers of Behçet: A Rare Disease?

   • Agata Polizzi, Domenica Taruscio

   Pages 1-4

3. From Hippocrates to Hulusi Behçet: What History

   • Donatella Lippi

   Pages 5-15

4. Epidemiology of Behçet Syndrome

   • Olga Addimanda, Giulia Pazzola, Nicolò Pipitone, Carlo Salvarani

   Pages 17-24

5. Behçet’s Syndrome According to Classical and Population Genetics

   • Akira Meguro, Nobuhisa Mizuki, Ahmet Gül, Nobuyoshi Kitaichi, Shigeaki Ohno

   Pages 25-37

6. Infections, Autoimmunity, and Behçet’s Syndrome: What Liaison?

   • Mario Milco D’Elios, Marisa Benagiano, Amedeo Amedei, Giacomo Emmi

   Pages 39-51

7. Pathogenesis of Behçet Syndrome

   • Giacomo Emmi, Danilo Squatrito, Elena Silvestri, Alessia Grassi, Lorenzo Emmi

   Pages 53-66

8. Mucocutaneous Involvement in Behçet’s Syndrome

   • Umit Tursen

   Pages 67-81

9. Neurological and Neuropsychological Manifestation in Behçet’s Syndrome

   • Shunsei Hirohata

   Pages 83-96

10. Ocular Involvement and Behçet Disease

    • Lorenzo Vannozzi, Ugo Menchini, Massimo Accorinti

    Pages 97-115

11. Articular and Muscular Manifestations in Behçet’s Disease

    • Anne-Claire Desbois, Betrand Wechsler, David Saadoun

    Pages 117-123

12. Cardiovascular Issues: Aneurysms and Pseudoaneurysms, Thrombosis, Atherosclerosis, and Cardiac Involvement

    • Elena Silvestri, Caterina Cenci, Chiara Della Bella, Anna Maria Cameli, Domenico Prisco

    Pages 125-135

13. Intestinal Behçet Disease

    • Cristina Cenci, Monica Milla

    Pages 137-149

14. Audio Vestibular Involvement in Behçet’s Disease

    • Paolo Vannucchi, Rudi Pecci

    Pages 151-153

15. Behçet’s Syndrome and Gynecological Manifestation in Reproductive Age and Pregnancy

    • Maria Elisabetta Coccia, Tommaso Capezzuoli

    Pages 155-164

16. Pediatric Onset of Behçet Syndrome

    • Ezgi Deniz Batu, Rolando Cimaz, Seza Özen

    Pages 165-176

17. Behçet’s Disease. Differential Diagnosis

    • Maria Grazia Sabbadini, Stefano Franchini

    Pages 177-188

18. Classification and Diagnosis Criteria for Behçet’s Disease

    • Fereydoun Davatchi, Bahar Sadeghi Abdollahi, Farhad Shahram, Cheyda Chams-Davatchi, Hormoz Shams, Abdolhadi Nadji

    Pages 189-198

19. Prognosis and Disease Activity

    • Rosaria Talarico, Anna d’Ascanio, Rossella Neri, Chiara Baldini, Marta Mosca, Stefano Bombardieri

    Pages 199-205

20. Old and New Treatment for Behçet’s Disease

    • Fabrizio Cantini, Gerardo Di Scala

    Pages 207-216

Behçet's syndrome can reasonably be considered a unique entity among diseases of the immune system for several reasons: It has specific features and, uniquely among the immune system pathologies, represents a link between autoimmune diseases, systemic vasculitis, and autoinflammatory diseases. In addition, it is of interest to a variety of specialists, including immunologists, rheumatologists, dermatologists, and ophthalmologists, and requires a complex multidisciplinary approach. Many aspects need to be considered in a syndrome that presents a wide spectrum of symptoms and for which the therapeutic armamentarium is expanding significantly, with the development of new treatments, not least the so-called biologics. This book offers comprehensive coverage of the disease by some of the world’s leading experts in Behçet's syndrome from all the relevant specialties. Epidemiology, genetics, pathogenesis, organ system involvement, differential diagnosis, novel treatments, surgical management,and prognosis are just some of the topics addressed. Behçet's Syndrome: From Pathogenesis to Treatment will be an invaluable reference for a range of practitioners, researchers, and undergraduates or postgraduates interested in immuno-rheumatology, dermatology, and rare diseases.​    

• Autoimmune disease
• Autoinflammatory disease
• Behçet's syndrome
• Rare disease
• Vasculitis

From the book reviews:

“This collection meets the objective of bringing information on Behcet’s syndrome together in one place, and is the most recent of all efforts to do so. It is most appropriate for rheumatologists and other subspecialists who are treating these patients and who are interested in reviewing the clinical characteristics of this protean disorder, as this information makes up the bulk of the book.” (Tiphanie Vogel, Doody’s Book Reviews, September, 2014)

• SOD Patologia Medica, Center for Autoimmune Systemic Diseases, Behçet Center and Lupus Clinic - AOU Careggi, Florence, Italy

  Lorenzo Emmi

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